CATH Classification

Domain Context

CATH Clusters

Superfamily Immunoglobulins
Functional Family Alpha-L-iduronidase

Enzyme Information

3.2.1.76
L-iduronidase.
based on mapping to UniProt P35475
Hydrolysis of unsulfated alpha-L-iduronosidic linkages in dermatan sulfate.

UniProtKB Entries (1)

P35475
IDUA_HUMAN
Homo sapiens
Alpha-L-iduronidase

PDB Structure

PDB 3W81
External Links
Method X-RAY DIFFRACTION
Organism
Primary Citation
Human alpha-L-iduronidase uses its own N-glycan as a substrate-binding and catalytic module
Maita, N., Tsukimura, T., Taniguchi, T., Saito, S., Ohno, K., Taniguchi, H., Sakuraba, H.
Proc.Natl.Acad.Sci.USA