PDB Information

PDB3O10
MethodX-RAY DIFFRACTION
Host OrganismEscherichia coli
Gene SourceHomo sapiens
Primary Citation
Structural basis of defects in the sacsin HEPN domain responsible for autosomal recessive spastic ataxia of Charlevoix-Saguenay (ARSACS).
Kozlov, G., Denisov, A.Y., Girard, M., Dicaire, M.J., Hamlin, J., McPherson, P.S., Brais, B., Gehring, K.
J.Biol.Chem.
HeaderChaperone
Released2010-07-20
Resolution1.900
CATH Insert Date03 Apr, 2011

PDB Images (9)

PDB Prints

PDB Chains (4)

Chain ID Date inserted into CATH CATH Status
A 04 Apr, 2011 Chopped
B 04 Apr, 2011 Chopped
C 04 Apr, 2011 Chopped
D 04 Apr, 2011 Chopped

CATH Domains (4)

Domain ID Date inserted into CATH Superfamily CATH Status
3o10A00 18 Mar, 2013 1.20.120.330 Assigned
3o10B00 18 Mar, 2013 1.20.120.330 Assigned
3o10C00 18 Mar, 2013 1.20.120.330 Assigned
3o10D00 18 Mar, 2013 1.20.120.330 Assigned

UniProtKB Entries (4)

Accession Gene ID Taxon Description
Q9NZJ4 SACS_HUMAN Homo sapiens Sacsin
Q9NZJ4 SACS_HUMAN Homo sapiens Sacsin
Q9NZJ4 SACS_HUMAN Homo sapiens Sacsin
Q9NZJ4 SACS_HUMAN Homo sapiens Sacsin