CATH Classification

Domain Context

CATH Clusters

Superfamily Frataxin/CyaY
Functional Family Frataxin, mitochondrial

Enzyme Information

1.16.3.1
Ferroxidase.
based on mapping to UniProt Q16595
4 Fe(2+) + 4 H(+) + O(2) = 4 Fe(3+) + 2 H(2)O.

UniProtKB Entries (1)

Q16595
FRDA_HUMAN
Homo sapiens
Frataxin, mitochondrial

PDB Structure

PDB 3S5F
External Links
Method X-RAY DIFFRACTION
Organism
Primary Citation
Friedreich's Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron-Sulfur Cluster Assembly Complex.
Tsai, C.L., Bridwell-Rabb, J., Barondeau, D.P.
Biochemistry