CATH Classification

Domain Context

CATH Clusters

Superfamily Golgi alpha-mannosidase II
Functional Family Alpha-galactosidase A

Enzyme Information

3.2.1.22
Alpha-galactosidase.
based on mapping to UniProt P06280
Hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha- D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids.
-!- Also hydrolyzes alpha-D-fucosides.

UniProtKB Entries (1)

P06280
AGAL_HUMAN
Homo sapiens
Alpha-galactosidase A

PDB Structure

PDB 3LXC
External Links
Method X-RAY DIFFRACTION
Organism
Primary Citation
Interconversion of the specificities of human lysosomal enzymes associated with Fabry and Schindler diseases.
Tomasic, I.B., Metcalf, M.C., Guce, A.I., Clark, N.E., Garman, S.C.
J.Biol.Chem.