CATH Classification

Domain Context

CATH Clusters

Superfamily 1.20.1280.180
Functional Family Carnitine O-palmitoyltransferase 2, mitochondrial

Enzyme Information

2.3.1.21
Carnitine O-palmitoyltransferase.
based on mapping to UniProt P18886
Palmitoyl-CoA + L-carnitine = CoA + L-palmitoylcarnitine.
-!- Broad specificity to acyl group, over the range C(8) to C(18); optimal activity with palmitoyl-CoA (cf. EC 2.3.1.7 and EC 2.3.1.137).

UniProtKB Entries (1)

P18886
CPT2_RAT
Rattus norvegicus
Carnitine O-palmitoyltransferase 2, mitochondrial

PDB Structure

PDB 2FW3
External Links
Method X-RAY DIFFRACTION
Organism Escherichia
Primary Citation
The crystal structure of carnitine palmitoyltransferase 2 and implications for diabetes treatment
Rufer, A.C., Thoma, R., Benz, J., Stihle, M., Gsell, B., De Roo, E., Banner, D.W., Mueller, F., Chomienne, O., Hennig, M.
Structure