CATH Classification

Domain Context

CATH Clusters

Superfamily Golgi alpha-mannosidase II
Functional Family Alpha-galactosidase A

Enzyme Information

3.2.1.22
Alpha-galactosidase.
based on mapping to UniProt P06280
Hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha- D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids.
-!- Also hydrolyzes alpha-D-fucosides.

UniProtKB Entries (1)

P06280
AGAL_HUMAN
Homo sapiens
Alpha-galactosidase A

PDB Structure

PDB 1R46
External Links
Method X-RAY DIFFRACTION
Organism Homo
Primary Citation
The molecular defect leading to Fabry disease: structure of human alpha-galactosidase
Garman, S.C., Garboczi, D.N.
J.Mol.Biol.