PDB 6cer
PDB Information
| PDB | 6CER |
| Method | X-RAY DIFFRACTION |
| Host Organism | Escherichia coli |
| Gene Source | Homo sapiens |
| Primary Citation | Pyruvate dehydrogenase complex deficiency is linked to regulatory loop disorder in the alpha V138M variant of human pyruvate dehydrogenase.
J. Biol. Chem.
|
| Header | Oxidoreductase |
| Released | 2018-02-12 |
| Resolution | 2.690 |
| CATH Insert Date | 16 Jul, 2018 |
PDB Images (21)
PDB Prints
PDB Chains (8)
| Chain ID | Date inserted into CATH | CATH Status |
|---|---|---|
| A | 16 Jul, 2018 | Chopped |
| B | 16 Jul, 2018 | Chopped |
| C | 16 Jul, 2018 | Chopped |
| D | 16 Jul, 2018 | Chopped |
| E | 16 Jul, 2018 | Chopped |
| F | 16 Jul, 2018 | Chopped |
| G | 16 Jul, 2018 | Chopped |
| H | 16 Jul, 2018 | Chopped |
CATH Domains (12)
| Domain ID | Date inserted into CATH | Superfamily | CATH Status |
|---|---|---|---|
| 6cerA00 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerB01 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerB02 | 19 Jul, 2018 | 3.40.50.920 | Assigned |
| 6cerC00 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerD01 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerD02 | 19 Jul, 2018 | 3.40.50.920 | Assigned |
| 6cerE00 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerF01 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerF02 | 19 Jul, 2018 | 3.40.50.920 | Assigned |
| 6cerG00 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerH01 | 19 Jul, 2018 | 3.40.50.970 | Assigned |
| 6cerH02 | 19 Jul, 2018 | 3.40.50.920 | Assigned |
UniProtKB Entries (8)
| Accession | Gene ID | Taxon | Description |
|---|---|---|---|
| P11177 | ODPB_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial |
| P08559 | ODPA_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial |
| P08559 | ODPA_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial |
| P11177 | ODPB_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial |
| P08559 | ODPA_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial |
| P11177 | ODPB_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial |
| P11177 | ODPB_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial |
| P08559 | ODPA_HUMAN | Homo sapiens | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial |
