PDB Information

PDB3HOR
MethodX-RAY DIFFRACTION
Host OrganismEscherichia coli
Gene SourceHomo sapiens
Primary Citation
Skeletal dysplasias due to filamin A mutations result from a gain-of-function mechanism distinct from allelic neurological disorders
Clark, A.R., Sawyer, G.M., Robertson, S.P., Sutherland-Smith, A.J.
Hum.Mol.Genet.
HeaderStructural Protein
Released2009-06-03
Resolution2.700
CATH Insert Date18 Oct, 2009

PDB Images (7)

PDB Prints

PDB Chains (2)

Chain ID Date inserted into CATH CATH Status
A 18 Oct, 2009 Chopped
B 18 Oct, 2009 Chopped

CATH Domains (4)

Domain ID Date inserted into CATH Superfamily CATH Status
3horA01 17 Feb, 2010 1.10.418.10 Assigned
3horA02 17 Feb, 2010 1.10.418.10 Assigned
3horB01 17 Feb, 2010 1.10.418.10 Assigned
3horB02 17 Feb, 2010 1.10.418.10 Assigned

UniProtKB Entries (2)

Accession Gene ID Taxon Description
P21333 FLNA_HUMAN Homo sapiens Filamin-A
P21333 FLNA_HUMAN Homo sapiens Filamin-A