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PDB Information
| PDB | 2GK1 |
| Method | X-RAY DIFFRACTION |
| Host Organism | |
| Gene Source | |
| Primary Citation |
Crystallographic Structure of Human beta-Hexosaminidase A: Interpretation of Tay-Sachs Mutations and Loss of G(M2) Ganglioside Hydrolysis.
Lemieux, M.J., Mark, B.L., Cherney, M.M., Withers, S.G., Mahuran, D.J., James, M.N.
J.Mol.Biol.
|
| Header | Hydrolase |
| Released | 2006-03-31 |
| Resolution | 3.250 |
| CATH Insert Date | 14 Jul, 2006 |
PDB Images (33)
2gk1I01
CATH Domain 2gk1I01
2gk1I02
CATH Domain 2gk1I02
2gk1J01
CATH Domain 2gk1J01
2gk1J02
CATH Domain 2gk1J02
2gk1K01
CATH Domain 2gk1K01
2gk1K02
CATH Domain 2gk1K02
2gk1L01
CATH Domain 2gk1L01
2gk1L02
CATH Domain 2gk1L02
2gk1N00
CATH Domain 2gk1N00
2gk1P00
CATH Domain 2gk1P00
2gk1R00
CATH Domain 2gk1R00
2gk1T00
CATH Domain 2gk1T00
PDB Chains (20)
| Chain ID | Date inserted into CATH | CATH Status |
| A | 14 Jul, 2006 | Holding pen
|
| B | 14 Jul, 2006 | Holding pen
|
| C | 14 Jul, 2006 | Holding pen
|
| D | 14 Jul, 2006 | Holding pen
|
| E | 14 Jul, 2006 | Holding pen
|
| F | 14 Jul, 2006 | Holding pen
|
| G | 14 Jul, 2006 | Holding pen
|
| H | 14 Jul, 2006 | Holding pen
|
| I | 14 Nov, 2017 | Chopped
|
| J | 14 Nov, 2017 | Chopped
|
| K | 14 Nov, 2017 | Chopped
|
| L | 14 Nov, 2017 | Chopped
|
| M | 14 Nov, 2017 | Holding pen
|
| N | 14 Nov, 2017 | Chopped
|
| O | 14 Nov, 2017 | Holding pen
|
| P | 14 Nov, 2017 | Chopped
|
| Q | 14 Nov, 2017 | Holding pen
|
| R | 14 Nov, 2017 | Chopped
|
| S | 14 Nov, 2017 | Holding pen
|
| T | 14 Nov, 2017 | Chopped
|
CATH Domains (12)
| Domain ID | Date inserted into CATH | Superfamily | CATH Status |
| 2gk1I01 | 16 Dec, 2017 | | Cathedral cath submit
|
| 2gk1I02 | 16 Dec, 2017 | 3.20.20.80 | Assigned
|
| 2gk1J01 | 16 Dec, 2017 | | Holding pen
|
| 2gk1J02 | 16 Dec, 2017 | 3.20.20.80 | Assigned
|
| 2gk1K01 | 16 Dec, 2017 | | Holding pen
|
| 2gk1K02 | 16 Dec, 2017 | 3.20.20.80 | Assigned
|
| 2gk1L01 | 16 Dec, 2017 | | Holding pen
|
| 2gk1L02 | 16 Dec, 2017 | 3.20.20.80 | Assigned
|
| 2gk1N00 | 16 Dec, 2017 | | Holding pen
|
| 2gk1P00 | 16 Dec, 2017 | | Holding pen
|
| 2gk1R00 | 16 Dec, 2017 | | Holding pen
|
| 2gk1T00 | 16 Dec, 2017 | | Holding pen
|
UniProtKB Entries (20)
| Accession |
Gene ID |
Taxon |
Description |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P06865 |
HEXA_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit alpha |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |
| P07686 |
HEXB_HUMAN |
Homo sapiens |
Beta-hexosaminidase subunit beta |