PDB Information

PDB1DTW
MethodX-RAY DIFFRACTION
Host OrganismEscherichia coli
Gene SourceHomo sapiens
Primary Citation
Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.
AEvarsson, A., Chuang, J.L., Wynn, R.M., Turley, S., Chuang, D.T., Hol, W.G.
Structure Fold.Des.
HeaderOxidoreductase
Released2000-01-13
Resolution2.700
CATH Insert Date05 Mar, 2006

PDB Images (6)

PDB Prints

PDB Chains (2)

Chain ID Date inserted into CATH CATH Status
A 05 Mar, 2006 Chopped
B 05 Mar, 2006 Chopped

CATH Domains (3)

Domain ID Date inserted into CATH Superfamily CATH Status
1dtwA00 05 Mar, 2006 3.40.50.970 Assigned
1dtwB01 05 Mar, 2006 3.40.50.920 Assigned
1dtwB02 05 Mar, 2006 3.40.50.970 Assigned

UniProtKB Entries (2)

Accession Gene ID Taxon Description
P21953 ODBB_HUMAN Homo sapiens 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
P12694 ODBA_HUMAN Homo sapiens 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial