PDB 1dtw
PDB Information
| PDB | 1DTW |
| Method | X-RAY DIFFRACTION |
| Host Organism | Escherichia coli |
| Gene Source | Homo sapiens |
| Primary Citation | Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.
Structure Fold.Des.
|
| Header | Oxidoreductase |
| Released | 2000-01-13 |
| Resolution | 2.700 |
| CATH Insert Date | 05 Mar, 2006 |
PDB Images (6)
PDB Prints
PDB Chains (2)
| Chain ID | Date inserted into CATH | CATH Status |
|---|---|---|
| A | 05 Mar, 2006 | Chopped |
| B | 05 Mar, 2006 | Chopped |
CATH Domains (3)
| Domain ID | Date inserted into CATH | Superfamily | CATH Status |
|---|---|---|---|
| 1dtwA00 | 05 Mar, 2006 | 3.40.50.970 | Assigned |
| 1dtwB01 | 05 Mar, 2006 | 3.40.50.920 | Assigned |
| 1dtwB02 | 05 Mar, 2006 | 3.40.50.970 | Assigned |
UniProtKB Entries (2)
| Accession | Gene ID | Taxon | Description |
|---|---|---|---|
| P21953 | ODBB_HUMAN | Homo sapiens | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial |
| P12694 | ODBA_HUMAN | Homo sapiens | 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial |
