CATH Classification

Domain Context

CATH Clusters

Superfamily Coproporphyrinogen III oxidase, aerobic
Functional Family oxygen-dependent coproporphyrinogen-III oxidase, mitochondrial

Enzyme Information

1.3.3.3
Coproporphyrinogen oxidase.
based on mapping to UniProt P36551
Coproporphyrinogen-III + O(2) + 2 H(+) = protoporphyrinogen-IX + 2 CO(2) + 2 H(2)O.

UniProtKB Entries (1)

P36551
HEM6_HUMAN
Homo sapiens
Oxygen-dependent coproporphyrinogen-III oxidase, mitochondrial

PDB Structure

PDB 2AEX
External Links
Method X-RAY DIFFRACTION
Organism Escherichia
Primary Citation
Structural basis of hereditary coproporphyria.
Lee, D.S., Flachsova, E., Bodnarova, M., Demeler, B., Martasek, P., Raman, C.S.
Proc.Natl.Acad.Sci.USA